Cystic fibrosis
Cystic Fibrosis Pulmonary Exacerbation Management I. What every physician needs to know. Cystic fibrosis (CF) is an autosomal recessive multi-system genetic disease characterized by abnormal transport of chloride and sodium across epithelium, leading to thick, viscous secretions in the sinuses, lungs, pancreas, liver, and intestine (See Figure 1). This comes in the form of: Figure…